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宫内磁共振成像在脊髓脊膜膨出管理中的作用

The role of intrauterine magnetic resonance in the management of myelomenigocele.

作者信息

Trigubo Denise, Negri Mercedes, Salvatico Rosana Mabel, Leguizamón Gustavo

机构信息

High Risk Pregnancy Unit, Department of Obstetrics & Gynecology, C.E.M.I.C. University, Buenos Aires, Argentina.

Department of Radiology (FLENI), Centro Diagnostico Rossi and Medical Institution Dr Pedro Lylyk, Buenos Aires, Argentina.

出版信息

Childs Nerv Syst. 2017 Jul;33(7):1107-1111. doi: 10.1007/s00381-017-3418-x. Epub 2017 May 17.

DOI:10.1007/s00381-017-3418-x
PMID:28516216
Abstract

OBJECTIVE

To assess the role of magnetic resonance imaging (MRI) in the management of myelomenigocele.

BACKGROUND

Spinal dysraphism or neural tube defects (NTD) encompass a heterogeneous group of congenital spinal anomalies that result from the defective closure of the neural tube early in gestation. Myelomeningocele is the most common type of NTD that is compatible with life, with high survival rates but lifelong physical impairments.

CONCLUSION

MRI is an important adjunct to ultrasound in assessing NTD, as it pertains to pre-surgical planning and perinatal management. However, it should not be considered a replacement for ultrasonography, which continues to be the gold standard for fetal anatomic evaluation.

摘要

目的

评估磁共振成像(MRI)在脊髓脊膜膨出管理中的作用。

背景

脊柱裂或神经管缺陷(NTD)包括一组异质性的先天性脊柱异常,这些异常是由于妊娠早期神经管闭合缺陷所致。脊髓脊膜膨出是最常见的一种可存活的NTD类型,存活率高但会导致终身身体残疾。

结论

MRI在评估NTD方面是超声的重要辅助手段,适用于术前规划和围产期管理。然而,不应将其视为超声检查的替代品,超声检查仍是胎儿解剖评估的金标准。

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本文引用的文献

1
Magnetic Resonance Imaging Evaluation of Fetal Neural Tube Defects.胎儿神经管缺陷的磁共振成像评估
Semin Ultrasound CT MR. 2015 Dec;36(6):487-500. doi: 10.1053/j.sult.2015.06.004. Epub 2015 Jun 16.
2
Fetal MRI: A Technical Update with Educational Aspirations.胎儿磁共振成像:兼具教育愿景的技术更新
Concepts Magn Reson Part A Bridg Educ Res. 2014 Nov;43(6):237-266. doi: 10.1002/cmr.a.21321.
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Diagnostic features of myelomeningocele: the role of ultrafast fetal MRI.脊髓脊膜膨出的诊断特征:超快胎儿磁共振成像的作用
Radiologe. 2018 Jul;58(7):659-663. doi: 10.1007/s00117-018-0401-9.
Fetal Diagn Ther. 2015;37(3):219-25. doi: 10.1159/000363738. Epub 2014 Jul 22.
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In utero repair of spina bifida.脊柱裂的宫内修复
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Prospects for fetal surgery.胎儿手术的前景。
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Spinal neural tube defects on in utero MRI.胎儿磁共振成像中的脊髓神经管缺陷。
Clin Radiol. 2013 Dec;68(12):e715-22. doi: 10.1016/j.crad.2013.07.019. Epub 2013 Sep 10.
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Prenatal diagnosis of spinal dysraphism.脊柱裂的产前诊断
Childs Nerv Syst. 2013 Sep;29(9):1541-52. doi: 10.1007/s00381-013-2178-5. Epub 2013 Sep 7.
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Magnetic resonance imaging in the prenatal diagnosis of neural tube defects.磁共振成像在神经管缺陷产前诊断中的应用。
Insights Imaging. 2013 Apr;4(2):225-37. doi: 10.1007/s13244-013-0223-2. Epub 2013 Mar 1.
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A randomized trial of prenatal versus postnatal repair of myelomeningocele.随机试验:产前与产后修复脊髓脊膜膨出。
N Engl J Med. 2011 Mar 17;364(11):993-1004. doi: 10.1056/NEJMoa1014379. Epub 2011 Feb 9.
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Cognitive and functional outcome in spina bifida-Chiari II malformation.脊柱裂- Chiari II 型畸形的认知和功能结局
Childs Nerv Syst. 2011 Jun;27(6):967-74. doi: 10.1007/s00381-010-1368-7. Epub 2010 Dec 31.