Arnaud Daniel, Varon Joseph, Surani Salim
Dorrington Medical Associates and Universidad Autonoma de Tamaulipas, Houston, TX, USA.
The University of Texas Health Science Center at Houston, Houston, TX 77030, USA.
Case Rep Pulmonol. 2017;2017:6719617. doi: 10.1155/2017/6719617. Epub 2017 Apr 24.
Congenital lobar emphysema is an uncommon bronchopulmonary malformation characterized by lobar overinflation and accompanying alveolar septum damage that leads to compression atelectasis of the lung parenchyma and displacement of mediastinal structures, with the resultant ventilation-perfusion mismatch. We present a case of a 33-year-old lady with progressive exertional dyspnea. Chest radiograph findings lead to the suspicion of congenital lobar emphysema, which was then confirmed by a computed tomography (CT) scan. This condition is most commonly identified in newborns, with very few cases being reported in adults. Lobectomy remains the treatment of choice and in general has good outcome.
先天性肺叶气肿是一种罕见的支气管肺畸形，其特征为肺叶过度充气以及伴随的肺泡间隔损伤，进而导致肺实质压迫性肺不张和纵隔结构移位，最终出现通气-灌注不匹配。我们报告一例33岁女性，有进行性劳力性呼吸困难。胸部X线片检查结果提示先天性肺叶气肿，随后经计算机断层扫描（CT）得以确诊。这种疾病在新生儿中最为常见，成人病例报道极少。肺叶切除术仍然是首选治疗方法，总体预后良好。
