Seo Chin Jin, Lek Sze Min, Tan Grace Hwei Ching, Teo Melissa
Singapore General Hospital, Singapore, Singapore.
SingHealth, Singapore, Singapore.
BMJ Case Rep. 2017 May 22;2017:bcr-2016-217887. doi: 10.1136/bcr-2016-217887.
Angiosarcomas account for only 1-2% of all soft tissue sarcomas, with the most common site of origin being in the head and neck region. Peritoneal angiosarcoma is an extremely rare tumour and few cases have been reported previously. Presentation of peritoneal angiosarcoma can be very variable, hence making diagnosis difficult. Herein, we review the current literature and describe a rare case of a patient who presented with haemorrhagic ascites, 17 years after radiotherapy for endometrial carcinoma and was subsequently diagnosed with peritoneal angiosarcoma. Due to extensive disease, surgery was not a viable option. She was started on palliative chemotherapy, but despite treatment, her condition deteriorated further and she eventually passed away. We highlight the diagnostic challenges and considerations in these patients as well as current treatment and management options available.
血管肉瘤仅占所有软组织肉瘤的1%-2%，最常见的起源部位是头颈部区域。腹膜血管肉瘤是一种极其罕见的肿瘤，此前仅有少数病例报道。腹膜血管肉瘤的表现差异很大，因此诊断困难。在此，我们回顾了当前的文献，并描述了一例罕见病例，该患者在子宫内膜癌放疗17年后出现血性腹水，随后被诊断为腹膜血管肉瘤。由于疾病广泛，手术不是一个可行的选择。她开始接受姑息化疗，但尽管进行了治疗，她的病情仍进一步恶化，最终去世。我们强调了这些患者的诊断挑战和注意事项，以及目前可用的治疗和管理选择。
