Gatti Arthur Paredes, Tonello Luiza, Pfaffenzeller William, Savóia Fernando Oliveira, Goergen Diego Inácio, De Pieri Coan Rodrigo, Teixeira Uirá Fernandes, Waechter Fábio Luiz, Fontes Paulo Roberto Ott
Departament of Surgery, Universidade Federal De Ciências Da Saúde De Porto Alegre (UFCSPA), Complexo Hospitalar Santa Casa de Porto Alegre, Porto Alegre, RS, 90050-170, Brazil.
Departament of Surgery, Universidade Federal De Ciências Da Saúde De Porto Alegre (UFCSPA), Complexo Hospitalar Santa Casa de Porto Alegre, Porto Alegre, RS, 90050-170, Brazil.
Int J Surg Case Rep. 2017;36:78-81. doi: 10.1016/j.ijscr.2017.04.029. Epub 2017 May 18.
Primary apocrine sweat gland carcinoma (PASGC) is an extremely rare neoplasia whose management and treatment are still evolving. The only curative therapy is wide local excision. Many patients have metastasis at the time of the diagnosis, mainly because this neoplasm has been misdiagnosed as some benign skin lesions.
We herein report a case of a 72-year-old-man with PASGC affecting the axilla and regional lymph nodes that underwent surgical resection and lymphadenectomy at our Institution. This is the first case reported in Brazil.
Our observation suggests just a MRI as necessary to study tumoral limits and lymph nodes and a full surgical excision with free margins is decisive for success.
Despite the PASGC be a rare cancer and require expensive tests, knowledge of this disease is critical to reduce costs in medical services without availability of investment.
原发性顶泌汗腺癌(PASGC)是一种极其罕见的肿瘤,其管理和治疗仍在不断发展。唯一的治愈性疗法是广泛局部切除。许多患者在诊断时已有转移,主要是因为这种肿瘤曾被误诊为一些良性皮肤病变。
我们在此报告一例72岁男性患有累及腋窝和区域淋巴结的PASGC,在我们机构接受了手术切除和淋巴结清扫术。这是巴西报道的首例病例。
我们的观察表明,仅需进行MRI以研究肿瘤边界和淋巴结,完整的切缘阴性手术切除对成功至关重要。
尽管PASGC是一种罕见癌症且需要昂贵的检查,但了解这种疾病对于在缺乏投资的情况下降低医疗服务成本至关重要。