Patil Priyanka, Tambe Swagata, Nayak Chitra, Ramya C
Department of Dermatology, Topiwala National Medical College and B.Y.L. Nair Hospital, Mumbai, Maharashtra, India.
Indian Dermatol Online J. 2017 May-Jun;8(3):195-197. doi: 10.4103/idoj.IDOJ_51_16.
Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue neoplasm of low-to-intermediate grade malignant potential. Childhood onset of DFSP is rare. It is most commonly seen on the trunk and proximal extremities. In children, a high index of suspicion is necessary to avoid delays in diagnosis that can lead to further morbidity. Here, we report a case of DFSP in a 9-year-old female child. Excision biopsy of lesion was performed with 1 cm margin. After confirmation of the diagnosis by histopathology, the patient was observed for recurrence, but there was no recurrence after 1 and half years of follow up.
隆突性皮肤纤维肉瘤（DFSP）是一种罕见的软组织肿瘤，具有低至中度的恶性潜能。儿童期发病的DFSP较为罕见。它最常见于躯干和近端肢体。对于儿童，必须保持高度怀疑，以避免诊断延误导致进一步的发病。在此，我们报告一例9岁女童的DFSP病例。对病变进行了切除活检，切缘为1厘米。经组织病理学确诊后，对患者进行了复发观察，但随访1年半后未出现复发。
