Neblett Carlos, Appiah Kenneth, Jones Javier, Lawrence Tahjeme, Dawkins Shanna Kay, Crookendale Graeme, Thompson Rory
Division of Plastic & Reconstructive Surgery, Department of Surgery, Bustamante Hospital for Children, 5 Arthur Wint Drive, Kingston 5, JMAAW04, Jamaica.
Department of Pathology, University Hospital of the West Indies, Mona, Kingston 7, JMAAW15, Jamaica.
J Surg Case Rep. 2024 Feb 13;2024(2):rjae062. doi: 10.1093/jscr/rjae062. eCollection 2024 Feb.
Dermatofibrosarcoma protuberans is a rare low-grade sarcoma, which rarely metastasizes, but it is locally aggressive with a propensity to recur. It usually affects persons of African descent and is extremely rare in childhood with a favourable prognosis. We present a case of paediatric dermatofibrosarcoma protuberans to the midline of the lower back of a 9-year-old Afro-Caribbean boy who was biopsied with a 2-mm margin. After histological confirmation, a 4-cm margin was then performed. Surveillance for recurrence, though none has been seen thus far after 6-month follow-up, will be done for at least 5 years and possibly longer, given this is the first case of this nature ever seen in our institution and the Caribbean region.
隆突性皮肤纤维肉瘤是一种罕见的低级别肉瘤,很少发生转移,但具有局部侵袭性且容易复发。它通常影响非洲裔人群,在儿童期极为罕见,预后良好。我们报告一例9岁非洲加勒比裔男孩下背部中线的小儿隆突性皮肤纤维肉瘤病例,该病例活检时切缘为2毫米。组织学确诊后,进行了4厘米的切缘切除。尽管在6个月的随访后尚未发现复发情况,但鉴于这是我们机构和加勒比地区首例此类病例,将至少进行5年甚至更长时间的复发监测。