一名成人中多脾症、卡塔格内综合征、背侧胰腺发育不全与多囊肾病的巧合。
Coincidence of Polysplenia, Kartagener Syndrome, Dorsal Pancreas Agenesis, and Polycystic Kidney Disease in an Adult.
作者信息
Demir Mustafa Kemal, Furuncuoglu Yavuz
机构信息
Department of Radiology, Bahçeşehir University School of Medicine, Göztepe Medical Park Hospital, Istanbul, Turkey.
Department of Internal Medicine, Bahçeşehir University School of Medicine, Göztepe Medical Park Hospital, Istanbul, Turkey.
出版信息
Eurasian J Med. 2017 Jun;49(2):152-154. doi: 10.5152/eurasianjmed.2017.17067.
Abstract
Here we present the case of an adult male patient with the anomalies of polysplenia, Kartagener syndrome, dorsal pancreas agenesis, and adult polycystic kidney disease. Familiarity with this extremely rare coincidence may improve diagnostic accuracy and patient management.
摘要
在此，我们报告一例成年男性患者，其患有多脾畸形、卡塔格纳综合征、背侧胰腺发育不全和成人多囊肾病。熟悉这种极其罕见的巧合情况可能会提高诊断准确性和患者管理水平。
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Polysplenia syndrome with congenital agenesis of dorsal pancreas presenting as acute pancreatitis and the role of endoscopic ultrasonography in its diagnosis.多脾综合征合并背侧胰腺先天性缺如表现为急性胰腺炎及内镜超声检查在其诊断中的作用
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