Department of Radiology, University of Chicago, IL 60637, USA.
Clin Imaging. 2010 Nov-Dec;34(6):472-5. doi: 10.1016/j.clinimag.2009.11.011.
Polysplenia syndrome (PS) is rarely encountered in elderly. It is characterized by multiple spleens associated with various cardiac and gastrointestinal abnormalities including partial or complete agenesis of dorsal pancreas. Situs inversus totalis (SIT) is a rare congenital anomaly with mirror image of viscera combined with dextrocardia. Occurrence of SIT and PS in the same patient is exceedingly rare. We present the first case of adult PS with SIT accompanied with annular pancreas.
多脾综合征（PS）在老年人中很少见。其特征是多个脾脏与各种心脏和胃肠道异常相关，包括背侧胰腺部分或完全发育不全。全内脏转位（SIT）是一种罕见的先天性异常，伴有内脏镜像和右位心。同一患者同时发生 SIT 和 PS 极为罕见。我们报告首例成人 PS 合并 SIT 伴环形胰腺。
