Pandya Vaidehi K, Sutariya Harsh C, Gandhi Shruti P, Khemchandani Sajni I, Patel Himanshu V, Shah Maulin K
a Department of Radio Diagnosis and Imaging. , G.R. Doshi and K.M. Mehta Institute of Kidney Diseases and Research Centre (IKDRC) and Dr. H.L. Trivedi Institute of Transplantation Sciences (ITS) , Civil Hospital Campus , Asarwa, Ahmedabad , Gujarat , India.
b Department of Transplantation surgery and Urology , G.R. Doshi and K.M. Mehta Institute of Kidney Diseases and Research Centre (IKDRC) and Dr. H.L. Trivedi Institute of Transplantation Sciences (ITS) , Civil Hospital Campus , Asarwa, Ahmedabad , Gujarat , India.
Ren Fail. 2017 Nov;39(1):533-539. doi: 10.1080/0886022X.2017.1337584.
Renal lymphangiectasia is rarely reported benign renal disorder of lymphatic malformation. Though found incidentally; it presents with nonspecific symptoms and shows characteristic findings in radiological imaging studies.
Here, we report eight patients with symptoms, laboratory and imaging findings compatible with renal lymphangiectasia. This report describes clinical and laboratory characteristics, treatment, Imaging findings and outcome of a series of patients with renal lymphangiectasia and reviews the literature.
Eight patients (mean age 45 years, male:female ratio 3:1) from 1st January 2011 to 30th June 2016; showing renal lymphangiectasia as incidental finding on CT IVP were included in the series. Imaging and laboratory findings were reviewed. Two out of eight patients (25%) underwent aspiration of collection and laboratory findings confirmed the diagnosis of renal lymphangiectasia. Four out of eight patients (50%) did not undergo aspiration of fluid and were offered conservative treatment. Two out of eight patients (25%) were donors for renal transplantation who were managed conservatively.
Renal lymphangiectasia was diagnosed on CT IVP. In each case, where aspiration of collection fluid was offered, the laboratory diagnosis of renal lymphangiectasia was confirmed and patients were managed conservatively. However, large collection in one patient was relieved by percutaneous aspiration.
Renal lymphangiectasia can be diagnosed with CT scan and confirmed by laboratory tests. As it may be confused with other cystic lesions of kidney; proper diagnosis and exclusion of other differentials can be effectively offered by CT scan IVP, which can avoid unnecessary invasive treatment options.
肾淋巴管扩张症是一种罕见的良性淋巴管畸形性肾脏疾病。尽管通常是偶然发现,但它表现为非特异性症状,在放射影像学检查中显示出特征性表现。
在此,我们报告8例具有与肾淋巴管扩张症相符的症状、实验室检查及影像学表现的患者。本报告描述了一系列肾淋巴管扩张症患者的临床和实验室特征、治疗、影像学表现及预后,并对相关文献进行了综述。
纳入2011年1月1日至2016年6月30日期间的8例患者(平均年龄45岁,男女比例为3:1),这些患者在CT静脉肾盂造影(CT IVP)检查中偶然发现肾淋巴管扩张症。回顾了其影像学和实验室检查结果。8例患者中有2例(25%)接受了积液抽吸,实验室检查结果证实了肾淋巴管扩张症的诊断。8例患者中有4例(50%)未进行液体抽吸,接受了保守治疗。8例患者中有2例(25%)是肾移植供体,接受了保守治疗。
通过CT IVP诊断出肾淋巴管扩张症。在每例提供积液抽吸的病例中,实验室诊断均证实为肾淋巴管扩张症,患者接受了保守治疗。然而,1例患者的大量积液通过经皮抽吸得以缓解。
肾淋巴管扩张症可通过CT扫描诊断,并通过实验室检查得以证实。由于它可能与肾脏的其他囊性病变相混淆,CT扫描IVP能够有效提供正确的诊断并排除其他鉴别诊断,从而避免不必要的侵入性治疗选择。