Marroquín J A, Hernández A C, Pilkington J P, Saviatto A, Tabuenca M J, Estenoz J M
Servicio de Medicina Nuclear, Hospital Universitario 12 de Octubre , Madrid, España.
Servicio de Medicina Nuclear, Hospital Universitario 12 de Octubre , Madrid, España.
Rev Esp Med Nucl Imagen Mol (Engl Ed). 2018 Mar-Apr;37(2):110-113. doi: 10.1016/j.remn.2017.04.008. Epub 2017 Jun 23.
The case presented is a 25-year-old male with a malignant neuroectodermal tumour on the left chest wall (Askin tumour), treated with surgery after neoadyuvant chemotherapy and followed by consolidation chemotherapy. After 9 years of disease free survival, the patient developed an acute pulmonary embolism. The echocardiogram, thoracic CT, and cardiac MRI scans revealed a mass in the right atrium. Recurrence of an Askin tumour versus an atrium myxoma was suspected. F-FDG PET/CT showed an intense hypermetabolic right atrium mass with extension to the right ventricle highly suggestive of malignancy. The result of the histopathology examination after biopsy and subsequently exeresis of the right atrium mass was consistent with a metastasis of the primary tumour.
该病例为一名25岁男性，左胸壁患有恶性神经外胚层肿瘤（阿斯金瘤），新辅助化疗后接受手术治疗，随后进行巩固化疗。在无病生存9年后，患者发生急性肺栓塞。超声心动图、胸部CT和心脏MRI扫描显示右心房有一肿块。怀疑是阿斯金瘤复发还是心房黏液瘤。F-FDG PET/CT显示右心房有一强烈高代谢肿块，延伸至右心室，高度提示为恶性肿瘤。活检及随后切除右心房肿块后的组织病理学检查结果与原发肿瘤转移相符。
