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本文引用的文献

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Isolated cardiac sarcoidosis: A focused review of an under-recognized entity.孤立性心脏结节病:一个被低估的实体的重点综述。
J Nucl Cardiol. 2018 Aug;25(4):1136-1146. doi: 10.1007/s12350-016-0658-1. Epub 2016 Sep 9.
2
Cardiac sarcoidosis-state of the art review.心脏结节病——最新综述
Cardiovasc Diagn Ther. 2016 Feb;6(1):50-63. doi: 10.3978/j.issn.2223-3652.2015.12.13.
3
Efficacy and safety of implantable cardiac defibrillators for treatment of ventricular arrhythmias in patients with cardiac sarcoidosis.心脏肉瘤病患者室性心律失常的植入型心脏除颤器治疗的疗效和安全性。
Europace. 2013 Mar;15(3):347-54. doi: 10.1093/europace/eus316. Epub 2012 Sep 21.
4
Cardiac sarcoidosis: a comprehensive review.心脏结节病:全面综述。
Arch Med Sci. 2011 Aug;7(4):546-54. doi: 10.5114/aoms.2011.24118. Epub 2011 Sep 2.
5
Arrhythmias in cardiac sarcoidosis: diagnosis and treatment.心脏结节病性心律失常:诊断与治疗。
Curr Opin Cardiol. 2012 Mar;27(2):181-9. doi: 10.1097/HCO.0b013e32834e4c7c.
6
Clinical problem-solving. The beat goes on.临床问题解决。节奏仍在继续。
N Engl J Med. 2010 May 6;362(18):1721-6. doi: 10.1056/NEJMcps0801473.
7
Refractory ventricular tachycardia secondary to cardiac sarcoid: electrophysiologic characteristics, mapping, and ablation.心脏结节病继发难治性室性心动过速:电生理特征、标测与消融
Heart Rhythm. 2006 Aug;3(8):924-9. doi: 10.1016/j.hrthm.2006.03.031. Epub 2006 Mar 30.
8
The cardiologists' worst nightmare sudden death from "benign" ventricular arrhythmias.心脏病专家最可怕的噩梦——因“良性”室性心律失常导致的猝死。
J Am Coll Cardiol. 2005 Oct 4;46(7):1295-7. doi: 10.1016/j.jacc.2005.07.010.
9
Ventricular tachyarrhythmia associated with cardiac sarcoidosis: its mechanisms and outcome.与心脏结节病相关的室性快速性心律失常:其机制与转归
Clin Cardiol. 2004 Apr;27(4):217-22. doi: 10.1002/clc.4960270409.
10
Cardiac sarcoidosis masquerading as right ventricular dysplasia.伪装成右心室发育不良的心脏结节病。
Pacing Clin Electrophysiol. 2003 Jul;26(7 Pt 1):1498-503. doi: 10.1046/j.1460-9592.2003.t01-1-00217.x.

伪装成右心室流出道室性心动过速的孤立性心脏结节病。

Isolated cardiac sarcoidosis masquerading as right ventricular outflow tract ventricular tachycardia.

作者信息

Atreya Auras R, Patel Mitkumar, Sivalingam Senthil K, Stoenescu Mathias L

机构信息

University of Massachusetts Medical School-Baystate, Springfield, Massachusetts, USA.

出版信息

BMJ Case Rep. 2017 Jun 30;2017:bcr-2017-220604. doi: 10.1136/bcr-2017-220604.

DOI:10.1136/bcr-2017-220604
PMID:28667170
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5535213/
Abstract

A 67-year-old man with coronary artery disease (CAD) and left anterior descending artery (LAD) stent presented with symptomatic monomorphic ventricular tachycardia (VT) at a rate of 190 bpm requiring cardioversion. ECG showed left bundle branch block pattern and inferior axis, suggestive of a right ventricular outflow tract (RVOT) focus rather than left ventricular scar due to LAD territory myocardial infarction (MI). Echocardiography showed normal wall motion. Angiography revealed a patent mid-LAD stent. Cardiac MRI with delayed postcontrast sequence revealed several regions of hyperenhancement abnormality within the basal portion of the interventricular septum. Increased metabolic activity on positron emission tomography confirmed active inflammatory sarcoidosis.Although VTs in patients with prior CAD are likely to be related to either scar or ischaemia, alternative diagnoses (eg, infiltrative disorders, RVOT-VT, arrhythmogenic right ventricular cardiomyopathy) should be considered in patients with an apparent right ventricular focus on ECG.

摘要

一名67岁患有冠状动脉疾病(CAD)且左前降支动脉(LAD)置入支架的男性,出现症状性单形性室性心动过速(VT),心率为190次/分钟,需要进行心脏复律。心电图显示左束支传导阻滞图形及下轴,提示右心室流出道(RVOT)起源,而非由于LAD区域心肌梗死(MI)导致的左心室瘢痕。超声心动图显示室壁运动正常。血管造影显示LAD中段支架通畅。心脏磁共振成像延迟增强序列显示室间隔基底部有几个高增强异常区域。正电子发射断层扫描显示代谢活性增加,证实为活动性炎症性结节病。尽管既往有CAD的患者发生的VT可能与瘢痕或缺血有关,但对于心电图上明显提示右心室起源的患者,应考虑其他诊断(如浸润性疾病、RVOT-VT、致心律失常性右心室心肌病)。