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嗜铬细胞瘤诱发的心肌病酷似急性冠状动脉综合征。

Pheochromocytoma-Induced Cardiomyopathy Mimicking Acute Coronary Syndrome.

作者信息

Vilcant Viliane

出版信息

J Am Osteopath Assoc. 2017 Aug 1;117(8):537-540. doi: 10.7556/jaoa.2017.104.

DOI:10.7556/jaoa.2017.104
PMID:28759096
Abstract

Pheochromocytoma is a rare catecholamine-secreting tumor with a prevalence of 0.1% to 0.6% in hypertensive patients. The classic triad of symptoms is headache, palpitations, and diaphoresis, but clinical presentation varies greatly. Pheochromocytoma can also mimic acute coronary syndrome and heart failure. With surgical resection, appropriate preoperative medical therapy, and 10% malignancy rate, prognosis is usually good. In the present case, a patient presented to the emergency department with symptoms suggesting a non-ST-segment elevation myocardial infarction and was transferred to a tertiary medical center for a cardiac catheterization. No coronary artery disease was found. However, cardiomyopathy developed, which made pheochromocytoma difficult to diagnose at first glance.

摘要

嗜铬细胞瘤是一种罕见的分泌儿茶酚胺的肿瘤,在高血压患者中的患病率为0.1%至0.6%。经典的三联征症状是头痛、心悸和多汗,但临床表现差异很大。嗜铬细胞瘤也可类似急性冠状动脉综合征和心力衰竭。通过手术切除、适当的术前药物治疗以及10%的恶性率,预后通常良好。在本病例中,一名患者因提示非ST段抬高型心肌梗死的症状就诊于急诊科,并被转至三级医疗中心进行心脏导管插入术。未发现冠状动脉疾病。然而,出现了心肌病,这使得嗜铬细胞瘤乍一看难以诊断。

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Pheochromocytoma-Induced Cardiomyopathy Mimicking Acute Coronary Syndrome.嗜铬细胞瘤诱发的心肌病酷似急性冠状动脉综合征。
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引用本文的文献

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Prehospital Misdiagnosed Acute Coronary Syndrome-Incidence, Discriminating Features, and Differential Diagnoses.院前误诊的急性冠状动脉综合征——发病率、鉴别特征及鉴别诊断
Rev Cardiovasc Med. 2023 Mar 2;24(3):75. doi: 10.31083/j.rcm2403075. eCollection 2023 Mar.
2
Case Report: Pheochromocytoma in a 59-Year-Old Woman Presenting With Hypotension.病例报告:一名59岁女性以低血压为表现的嗜铬细胞瘤
Front Cardiovasc Med. 2021 Mar 11;8:648725. doi: 10.3389/fcvm.2021.648725. eCollection 2021.
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Cardiovascular Manifestations and Complications of Pheochromocytomas and Paragangliomas.
嗜铬细胞瘤和副神经节瘤的心血管表现及并发症
J Clin Med. 2020 Jul 30;9(8):2435. doi: 10.3390/jcm9082435.
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An atypical presentation of acute coronary syndrome.急性冠状动脉综合征的非典型表现。
J Thorac Dis. 2018 Aug;10(8):E616-E619. doi: 10.21037/jtd.2018.07.55.