Ramalho Ana Rita, Costa Susana, Silva Francisco, Donato Paulo, Franco Fátima, Pêgo Guilherme Mariano
Coimbra Hospital and University Center, Cardiology Department, Coimbra, Portugal.
Coimbra Hospital and University Center, Imaging Department, Coimbra, Portugal.
ESC Heart Fail. 2017 Aug;4(3):365-370. doi: 10.1002/ehf2.12139. Epub 2017 Apr 22.
Primary cardiac involvement in systemic sclerosis is common, often subclinical, and is associated with significant mortality. We report the case of a patient who developed autoimmune myocarditis at an early stage of systemic sclerosis, who completely recovered from cardiac dysfunction under optimal medical therapy for heart failure and immunosuppression. This challenging case aims at increasing awareness around the fact that the heart is a target organ of scleroderma disease. It also highlights the importance of screening and early diagnosis of cardiac involvement, because a timely treatment may impact the quality of life of these patients and improve their prognosis.
系统性硬化症中的原发性心脏受累很常见，通常为亚临床状态，且与显著的死亡率相关。我们报告了一例在系统性硬化症早期发生自身免疫性心肌炎的患者，该患者在针对心力衰竭的最佳药物治疗和免疫抑制治疗下，心脏功能障碍完全恢复。这个具有挑战性的病例旨在提高人们对心脏是硬皮病疾病靶器官这一事实的认识。它还强调了筛查和早期诊断心脏受累的重要性，因为及时治疗可能会影响这些患者的生活质量并改善其预后。
