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一名9岁男孩幼年型无肌病性皮肌炎的节段性叠加表现

Superimposed Segmental Manifestation of Juvenile Amyopathic Dermatomyositis in a 9-year-old Boy.

作者信息

Bulur Isil, Erdogan Hilal Kaya, Saracoglu Zeynep Nurhan, Happle Rudolf, Canaz Funda

机构信息

Department of Dermatology, Faculty of Medicine, Eskisehir Osmangazi University, Eskisehir, Turkey.

Department of Dermatology, Freiburg University Medical Center, Freiburg, Germany.

出版信息

Indian J Dermatol. 2017 Jul-Aug;62(4):440. doi: 10.4103/ijd.IJD_335_16.

Abstract

Dermatomyositis is a well-known autoimmune disorder. On the other hand, juvenile amyopathic dermatomyositis (JADM) occurs rather rarely. Here, we report an unusual case in a 9-year-old Turkish boy showing a unilateral linear inflammatory skin lesion that was followed, after 16 months, by the appearance of bilateral disseminated features JADM.

摘要

皮肌炎是一种众所周知的自身免疫性疾病。另一方面,青少年无肌病性皮肌炎(JADM)则较为罕见。在此,我们报告一例罕见病例,一名9岁土耳其男孩出现单侧线状炎症性皮肤病变,16个月后出现双侧播散性JADM特征。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f4d5/5527735/1d465b92f671/IJD-62-440a-g001.jpg

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