Esatoglu Sinem Nihal, Kutlubay Zekayi, Ucar Didar, Hatemi Ibrahim, Uygunoglu Ugur, Siva Aksel, Hatemi Gulen
Division of Rheumatology, Department of Internal Medicine.
Department of Dermatology.
J Multidiscip Healthc. 2017 Aug 14;10:309-319. doi: 10.2147/JMDH.S93681. eCollection 2017.
Behçet's syndrome (BS) is a multisystem vasculitis that presents with a variety of mucocutaneous manifestations such as oral and genital ulcers, papulopustular lesions and erythema nodosum as well as ocular, vascular, gastrointestinal and nervous system involvement. Although it occurs worldwide, it is especially prevalent in the Far East and around the Mediterranean Sea. Male gender and younger age at disease onset are associated with a more severe disease course. The management of BS depends on the severity of symptoms. If untreated, morbidity and mortality are considerably high in patients with major organ involvement. Multidisciplinary patient care is essential for the management of BS, as it is for other multisystem diseases. Rheumatologists, dermatologists, ophthalmologists, neurologists, cardiovascular surgeons and gastroenterologists are members of the multidisciplinary team. In this study, we reviewed the epidemiology, etiology, diagnostic criteria sets, clinical findings and treatment of BS and highlighted the importance of the multidisciplinary team in the management of BS.
白塞病（BS）是一种多系统血管炎，表现为多种皮肤黏膜表现，如口腔和生殖器溃疡、丘疹脓疱性病变和结节性红斑，以及眼部、血管、胃肠道和神经系统受累。虽然该病在全球范围内均有发生，但在远东地区和地中海周围尤为普遍。男性以及发病时年龄较轻与更严重的病程相关。白塞病的治疗取决于症状的严重程度。如果不进行治疗，主要器官受累的患者发病率和死亡率相当高。与其他多系统疾病一样，多学科患者护理对白塞病的管理至关重要。风湿科医生、皮肤科医生、眼科医生、神经科医生、心血管外科医生和胃肠病科医生是多学科团队的成员。在本研究中，我们回顾了白塞病的流行病学、病因、诊断标准集、临床表现和治疗，并强调了多学科团队在白塞病管理中的重要性。
