Johnson Eric D, Downs-Kelly Erinn, Bull David A, Gulbahce H Evin
Department of Internal Medicine, University of Utah School of Medicine, Salt Lake City, Utah, USA.
Department of Pathology, Cleveland Clinic Foundation, Cleveland, Ohio, USA.
Case Rep Oncol. 2017 Jul 14;10(2):660-665. doi: 10.1159/000478845. eCollection 2017 May-Aug.
Primary pleuropulmonary synovial sarcomas are quite rare, representing 0.1-0.5% of all pulmonary malignancies. We report an entirely cystic monophasic synovial sarcoma in a 25-year-old male who presented with recurrent pneumothorax and no evidence of a mass lesion on imaging. The purpose of this case report is to increase awareness of neoplasms clinically presenting as a pneumothorax with no imagining evidence of a mass-forming lesion and emphasize the significance of fluorescent in situ hybridization testing in nontypical synovial sarcoma cases.
原发性胸膜肺滑膜肉瘤非常罕见,占所有肺恶性肿瘤的0.1%-0.5%。我们报告一例25岁男性的完全囊性单相滑膜肉瘤,该患者表现为复发性气胸,影像学检查未发现肿块病变。本病例报告的目的是提高对临床上表现为气胸但无肿块形成病变影像学证据的肿瘤的认识,并强调荧光原位杂交检测在非典型滑膜肉瘤病例中的重要性。