Marback Eduardo F, Espinheira Fonseca Luciano, Marback Roberto L
Federal University of Bahia, Salvador da Bahia, Brazil.
Ocul Oncol Pathol. 2017 Jul;3(2):110-112. doi: 10.1159/000451058. Epub 2016 Nov 9.
The aim of this paper was to report a rare presentation of adenoid cystic carcinoma.
This is a case report presenting clinical, radiographic, and histopathologic findings.
A 72-year-old female with no reported ocular symptoms was found to have an incidental right orbital mass on imaging. Additional studies revealed multiple liver lesions, which were biopsied and found to be consistent with adenoid cystic carcinoma. She was then referred to the ophthalmology service, where ocular examination demonstrated 2.5 mm of right proptosis with elevation and abduction deficits. Diplopia could be elicited in extreme upgaze and right lateral gaze. An excisional biopsy of the orbital mass was performed, with histopathology confirming the diagnosis of primary adenoid cystic carcinoma of the lacrimal gland, thereby also supporting the initial suspicion that the hepatic adenoid cystic carcinoma lesions represented metastases.
The authors describe a rare presentation of adenoid cystic carcinoma of the lacrimal gland, initially asymptomatic, with metastatic lesions restricted to the liver at the time of diagnosis. Three previous cases of adenoid cystic carcinoma with isolated metastatic hepatic lesions at the time of diagnosis have been reported; all of these cases localized the primary tumor to the salivary glands.
本文旨在报告腺样囊性癌的一种罕见表现。
这是一篇病例报告，呈现了临床、影像学和组织病理学检查结果。
一名72岁女性，无眼部症状报告，影像学检查偶然发现右侧眶内肿块。进一步检查发现多个肝脏病变，经活检发现与腺样囊性癌相符。随后她被转诊至眼科，眼部检查显示右眼眼球突出2.5毫米，伴有上抬和外展功能障碍。极度向上注视和右侧注视时可引出复视。对眶内肿块进行了切除活检，组织病理学确诊为泪腺原发性腺样囊性癌，这也支持了最初的怀疑，即肝脏腺样囊性癌病变为转移瘤。
作者描述了泪腺腺样囊性癌的一种罕见表现，最初无症状，诊断时转移灶局限于肝脏。此前已报道过3例诊断时伴有孤立性肝脏转移病变的腺样囊性癌病例；所有这些病例的原发肿瘤均位于唾液腺。
