半侧阴囊发育不全：一种罕见的先天性异常。
Hemiscrotal Agenesis: A Rare Congenital Anomaly.
作者信息
Psarris Alexandros, Dimopoulou Anastasia, Iakomidis Emmanouil, Zavras Nikolaos, Vaos Georgios
机构信息
Resident, Department of Gynaecology, Agios Savvas Cancer Hospital, Athens, Greece.
Consultant, Department of Paediatric Surgery, Attikon University General Hospital, School of Medicine, National and Kapodistrian University of Athens, Athens, Greece.
出版信息
J Clin Diagn Res. 2017 Aug;11(8):PD19-PD20. doi: 10.7860/JCDR/2017/28605.10507. Epub 2017 Aug 1.
Abstract
Hemiscrotal Agenesis (HSA) is the rarest developmental malformation of the scrotum. It is characterized by the absence of either half of the scrotal rugae with an intact midline raphe. We report the case of a 16-month-old boy with HSA, with an island of scrotal tissue in the pubic tubercle region and ipsilateral cryptorchidism. To our knowledge, this is the first case of HSA with heterotopic development of scrotal tissue.
摘要
半侧阴囊发育不全（HSA）是阴囊最罕见的发育畸形。其特征是阴囊皱襞的一半缺失，中线缝襞完整。我们报告一例16个月大患有HSA的男孩病例，其耻骨结节区域有一片阴囊组织岛，同侧存在隐睾。据我们所知，这是首例伴有阴囊组织异位发育的HSA病例。
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