Ernst Sabine, Roy Karine, Lim Eric, Thomas Glyn
Department of Cardiology, Royal Brompton Hospital, London, UK.
NIHR Cardiovascular Biomedical Research Unit, Royal Brompton and National Heart and Lung Institute, Imperial College London, London, UK.
Glob Cardiol Sci Pract. 2016 Dec 30;2016(4):e201639. doi: 10.21542/gcsp.2016.39.
Arrhythmogenic right ventricular dysplasia (ARVD) is an inheritable heart muscle disease that predominantly affects the right ventricle (RV) and predisposes to ventricular arrhythmias and sudden cardiac death (SCD). The natural history is predominantly related to ventricular electric instability which may lead to arrhythmic SCD, mostly in young people and athletes, but may progress with significant RV muscle disease and left-ventricular (LV) involvement and can result in right or biventricular heart failure. We report on a 54-year-old male with ARVD who underwent an epicardial ventricular tachycardia (VT) ablation using remote magnetic navigation (RMN) after functional imaging from a nuclear perfusion study was fused with a 3D segmentation from computed tomography (CT) imaging.
致心律失常性右室心肌病(ARVD)是一种遗传性心肌疾病,主要影响右心室(RV),易引发室性心律失常和心源性猝死(SCD)。其自然病程主要与心室电不稳定有关,这可能导致心律失常性SCD,多见于年轻人和运动员,但也可能随着显著的右室肌肉疾病和左心室(LV)受累而进展,进而导致右心或双心室心力衰竭。我们报告了一名54岁患有ARVD的男性患者,在将核灌注研究的功能成像与计算机断层扫描(CT)成像的三维分割融合后,使用远程磁导航(RMN)对其进行了心外膜室性心动过速(VT)消融。