左心室心肌致密化不全与复发性多形性室性心动过速：一例报告及文献复习
Left Ventricular Noncompaction Cardiomyopathy and Recurrent Polymorphic Ventricular Tachycardia: A Case Report and Literature Review.
作者信息
Akinseye Oluwaseun A, Ibebuogu Uzoma N, Jha Sunil K
机构信息
Cardiology Fellow at the University of Tennessee Health Science Center College of Medicine in Memphis.
Associate Professor of Cardiovascular Diseases at the University of Tennesse Health Science Center College of Medicine in Memphis.
出版信息
Perm J. 2017;21:17-045. doi: 10.7812/TPP/17-045.
Abstract
INTRODUCTION
Noncompaction cardiomyopathy is a rare phenotype of cardiomyopathy associated with severe cardiac arrhythmia and thromboembolic complications.
CASE PRESENTATION
A 55-year-old woman presented with frank pulmonary edema and received a diagnosis of noncompaction cardiomyopathy.
DISCUSSION
Left ventricular noncompaction cardiomyopathy is increasingly being diagnosed because of advances in imaging modalities. It is important to differentiate this new phenotype of cardiomyopathy from others because its diagnosis, management, and prognosis differ. We reviewed the literature and summarized the diagnostic criteria, associated complications, initial and long-term management, and the recommendation for family screening.
摘要
引言
致密化不全型心肌病是一种罕见的心肌病表型，与严重心律失常和血栓栓塞并发症相关。
病例介绍
一名55岁女性因明显肺水肿就诊，被诊断为致密化不全型心肌病。
讨论
由于影像学技术的进步，左心室致密化不全型心肌病的诊断越来越多。将这种新的心肌病表型与其他类型区分开来很重要，因为其诊断、管理和预后有所不同。我们回顾了文献并总结了诊断标准、相关并发症、初始和长期管理以及家族筛查建议。
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