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并存的胸腺和肺类癌肿瘤与1型多发性内分泌肿瘤相关

Coexisting Thymic and Pulmonary Carcinoid Tumors Associated with Multiple Endocrine Neoplasia Type1.

作者信息

Motoishi Makoto, Horimoto Kanna, Hayashi Kazuki, Sawai Satoru, Moriyoshi Koki

机构信息

Department of Thoracic Surgery, National Hospital Organization Kyoto Medical Center, Kyoto, Kyoto, Japan.

Department of Pathology, National Hospital Organization Kyoto Medical Center, Kyoto, Kyoto, Japan.

出版信息

Ann Thorac Cardiovasc Surg. 2018 Jun 20;24(3):147-150. doi: 10.5761/atcs.cr.17-00042. Epub 2017 Oct 26.

DOI:10.5761/atcs.cr.17-00042
PMID:29070772
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6033522/
Abstract

An anterior mediastinal tumor was detected in a 45-year-old female during a medical checkup. Chest computed tomography (CT) showed the anterior mediastinal tumor and a pulmonary tumor in the right lower lobe. Furthermore, tumors of the parathyroid gland, pancreas, and pituitary gland were also detected. She was clinically diagnosed with multiple endocrine neoplasia type1 (MEN1). The patient underwent extended thymectomy combined with mediastinal lymph node dissection and wedge resection of the lung including the right pulmonary lesion via a median sternotomy. We diagnosed the patient with an atypical carcinoid tumor of the thymus, a typical pulmonary carcinoid tumor.

摘要

一名45岁女性在体检时发现前纵隔肿瘤。胸部计算机断层扫描(CT)显示前纵隔肿瘤和右下叶肺部肿瘤。此外,还检测到甲状旁腺、胰腺和垂体的肿瘤。她被临床诊断为1型多发性内分泌肿瘤(MEN1)。患者通过正中胸骨切开术接受了扩大胸腺切除术,同时进行纵隔淋巴结清扫和包括右肺病变在内的肺楔形切除术。我们诊断该患者患有胸腺非典型类癌肿瘤,一种典型的肺类癌肿瘤。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6b4f/6033522/9f9e795e0ee1/atcs-24-147-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6b4f/6033522/7c60b6b90685/atcs-24-147-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6b4f/6033522/27f6a71f875c/atcs-24-147-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6b4f/6033522/9f9e795e0ee1/atcs-24-147-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6b4f/6033522/7c60b6b90685/atcs-24-147-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6b4f/6033522/27f6a71f875c/atcs-24-147-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6b4f/6033522/9f9e795e0ee1/atcs-24-147-g003.jpg

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引用本文的文献

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Simultaneous surgical resection of cardiac myxoma and atypical thymic carcinoid: a case report.心脏黏液瘤和非典型胸腺癌同期手术切除:一例报告。
J Med Case Rep. 2021 Oct 6;15(1):491. doi: 10.1186/s13256-021-03091-y.

本文引用的文献

1
Thymic neuroendocrine carcinoma (carcinoid) in multiple endocrine neoplasia type 1 syndrome: the Italian series.多发性内分泌腺瘤病1型综合征中的胸腺神经内分泌癌(类癌):意大利病例系列
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Bronchopulmonary carcinoid in multiple endocrine neoplasia type 1.1型多发性内分泌肿瘤中的支气管肺类癌
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Prospective study of thymic carcinoids in patients with multiple endocrine neoplasia type 1.
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Thymic carcinoid in a patient with multiple endocrine neoplasia type 1: report of a case.1型多发性内分泌腺瘤病患者的胸腺类癌:1例报告
Surg Today. 2001;31(5):428-32. doi: 10.1007/s005950170134.
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