Ahmad Zubair, Uddin Nasir, Memon Wasim, Abdul-Ghafar Jamshid, Ahmed Arsalan
Department of Pathology and Laboratory Medicine, Aga Khan University Hospital, Karachi, Pakistan.
Department of Radiology, Aga Khan University Hospital, Karachi, Pakistan.
J Med Case Rep. 2017 Nov 10;11(1):317. doi: 10.1186/s13256-017-1481-2.
Intrahepatic biliary cystadenomas are rare hepatic neoplasms, which are usually cystic. These tumors are often misdiagnosed as simple liver cysts and hydatid cysts clinically and radiologically owing to nonspecific clinical and radiologic features. These tumors require complete resection, as recurrence and malignant transformation can occur following incomplete excision. It is essential that these tumors be diagnosed accurately so that they can be adequately excised.
Clinical and radiological features of six cases of biliary cystadenoma are described.
All of these cases were resected with the clinical and/or radiological impression of simple liver cysts and/or hydatid cysts. Out of the six patients, five were female and one was male. Ages of the patients ranged from 28 to 60 years (mean 45 years). The patients presented with nonspecific symptoms. Internal septations were seen on preoperative imaging (when available). On gross examination, all tumors were cystic; their sizes varied from 5.5 to 14 cm, mean size was 9.0 cm. On histopathologic examination, cystic spaces were lined by cuboidal to columnar mucin-secreting epithelium with underlying ovarian-type stroma. In one case, ovarian-type stroma was not seen. Recurrence was seen in three cases at 1 to 5 years of follow up.
Owing to their malignant potential and high recurrence rate following incomplete resection, an aggressive surgical approach is recommended. Prognosis is excellent after complete resection.
肝内胆管囊腺瘤是一种罕见的肝脏肿瘤,通常为囊性。由于其临床和影像学特征不具有特异性,这些肿瘤在临床和影像学上常被误诊为单纯性肝囊肿和包虫囊肿。这些肿瘤需要完整切除,因为不完全切除后可能会复发和恶变。准确诊断这些肿瘤以便能够进行充分切除至关重要。
描述了6例胆管囊腺瘤的临床和影像学特征。
所有这些病例在临床和/或影像学上均被误诊为单纯性肝囊肿和/或包虫囊肿而进行了切除。6例患者中,5例为女性,1例为男性。患者年龄在28至60岁之间(平均45岁)。患者表现出非特异性症状。术前影像学检查(如有)可见内部间隔。大体检查时,所有肿瘤均为囊性;大小从5.5至14厘米不等,平均大小为9.0厘米。组织病理学检查显示,囊腔内衬有立方状至柱状分泌粘蛋白的上皮细胞,其下为卵巢型间质。有1例未见到卵巢型间质。随访1至5年,3例出现复发。
由于其具有恶变潜能且不完全切除后复发率高,建议采取积极的手术方法。完整切除后预后良好。