Myoteri D, Dellaportas D, Nastos C, Gioti I, Gkiokas G, Carvounis E, Theodosopoulos T
Pathology Department, Aretaieion University Hospital, Medical School of Athens, Athens, Greece.
2nd Department of Surgery, Aretaieion University Hospital, Medical School of Athens, Athens, Greece.
Case Rep Oncol Med. 2017;2017:4634235. doi: 10.1155/2017/4634235. Epub 2017 Sep 12.
Solitary fibrous tumor is a rare type of mesenchymal, spindle-cell tumor reported mostly in the pleura. Retroperitoneal occurrence is rare and histopathological diagnosis is challenging.
A 55-year-old woman with nonspecific abdominal pain was found to have a retroperitoneal/pelvic mass adjacent to the upper rectum. The patient underwent surgical resection in clear margins of this pelvic tumor, entering the total mesenteric excision surgical plane. Final histopathology revealed a solitary fibrous tumor and the case is presented herein.
Solitary fibrous tumor in the retroperitoneum is rarely found in the literature and to the best of our knowledge less than a hundred cases are described so far. Histopathological diagnosis is mostly based on a "patternless pattern" on microscopic examination, which is a storiform arrangement of spindle cells combined with a "hemangiopericytoma-like appearance" and increased vascularity of the lesion. Surgery is the mainstay of treatment and recurrence rates are generally low.
孤立性纤维瘤是一种罕见的间叶性梭形细胞瘤，主要见于胸膜。腹膜后发生罕见，组织病理学诊断具有挑战性。
一名55岁女性因非特异性腹痛就诊，发现直肠上段旁有一腹膜后/盆腔肿块。患者接受了该盆腔肿瘤的手术切除，切缘清晰，进入了全肠系膜切除手术平面。最终组织病理学检查显示为孤立性纤维瘤，现将该病例报告如下。
腹膜后孤立性纤维瘤在文献中很少见，据我们所知，迄今为止报道的病例不到100例。组织病理学诊断主要基于显微镜检查的“无模式模式”，即梭形细胞呈束状排列，伴有“血管外皮细胞瘤样外观”，且病变血管增多。手术是主要治疗方法，复发率一般较低。
