Jiang Shufen, Yin Xiaomeng, Dong Chang, Xia Yunlong, Liu Jinqiu
aDepartment of Cardiovascular medicine bDepartment of respiratory medicine, The First Affiliated Hospital of Dalian Medical University, Dalian, China.
Medicine (Baltimore). 2017 Nov;96(46):e8688. doi: 10.1097/MD.0000000000008688.
Brugada syndrome (BrS) is characterized by ST segment elevation at the J point ≥2 mm in the right precordial electrocardiogram (ECG) leads, in the absence of structural heart disease, electrolyte disturbances, or ischemia. It is a well-described cause of sudden death in young patients, especially in the age of between 30 and 40 years old. Here, we reported an unusual case of electrical storm (ES) of ventricular fibrillation (VF) caused by BrS with complete right bundle-branch block (CRBBB) in a 75-year-old male patient.
A 75-year-old male patient survived sudden cardiac death caused by a ventricular ES. He presented with the cove-shaped ST elevation of 2 mm in lead V1 with typical CRBBB and lacked structural cardiomyopathy and coronary heart disease. The patient suffered ventricular ES again, although the implantable cardioverter defibrillator(ICD) had implanted.
Brugada syndrome with complete right bundle-branch block.
Implantable cardioverter defibrillator (ICD) implantation was performed. But this therapy could not prevent the recurrence of malignant arrhythmia. Finally, the ES was treated successfully using radiofrequency catheter ablation (RFCA) at the area of the free wall of the right ventricular outflow tract (RVOT) epicardium.
During 7 months of follow-up, the patient was asymptomatic and free of arrhythmic events.
As far as we know, the patient is the oldest patient reported to have BrS. RFCA offers an alternative therapy for patients with BrS, especially when ICD shocks are encountered.
布加综合征(BrS)的特征是右胸前心电图(ECG)导联J点处ST段抬高≥2毫米,且无结构性心脏病、电解质紊乱或缺血。它是年轻患者,尤其是30至40岁患者猝死的常见原因。在此,我们报告了一例75岁男性患者因布加综合征合并完全性右束支传导阻滞(CRBBB)导致心室颤动(VF)电风暴(ES)的罕见病例。
一名75岁男性患者在经历了一次由心室电风暴导致的心脏骤停后幸存。他的心电图显示V1导联出现2毫米的穹窿形ST段抬高,并伴有典型的完全性右束支传导阻滞,且没有结构性心肌病和冠心病。尽管已植入植入式心律转复除颤器(ICD),但该患者再次发生心室电风暴。
布加综合征合并完全性右束支传导阻滞。
进行了植入式心律转复除颤器(ICD)植入。但该治疗无法预防恶性心律失常的复发。最终,通过在右心室流出道(RVOT)心外膜游离壁区域进行射频导管消融(RFCA)成功治疗了电风暴。
在7个月的随访期间,患者无症状,未发生心律失常事件。
据我们所知,该患者是报告的患有布加综合征的年龄最大的患者。射频导管消融术为布加综合征患者提供了一种替代治疗方法,尤其是在遇到ICD电击时。