Lu Liqing, Zhang Chunfang, Cheng Yuanda
Department of Thoracic Surgery, Xiangya Hospital, Central South University, Changsha 410008, China.
Zhongguo Fei Ai Za Zhi. 2017 Nov 20;20(11):787-788. doi: 10.3779/j.issn.1009-3419.2017.11.11.
We present a case of two-year old boy with solitary atypical adenomatous hyperplasia (AAH) in extralobar sequestration (ELS), which was misdiagnosed as diaphragmatic hernia before surgery. Review of AAH and pulmonary sequestration (PS) revealed that the present case is the youngest of solitary AAH and also the first report of solitary AAH arising in ELS without a primary lung cancer. In a sense, the present case firstly supports the hypothesis that ELS may be an underlying cancer predisposition syndrome, so aggressive surgical therapy should be recommended for ELS.
我们报告了一例2岁男孩，其在肺叶外隔离症（ELS）中出现孤立性非典型腺瘤样增生（AAH），术前被误诊为膈疝。对AAH和肺隔离症（PS）的回顾显示，本病例是孤立性AAH中最年轻的，也是首例ELS中出现的孤立性AAH且无原发性肺癌的报道。从某种意义上说，本病例首先支持了ELS可能是一种潜在的癌症易患综合征的假说，因此对于ELS应推荐积极的手术治疗。
