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一名患有艾森曼格综合征的17岁青少年晚期青光眼合并巩膜静脉压升高病例。

A Case of Advanced Glaucoma with Increased Episcleral Venous Pressure in a 17-Year-Old with Eisenmenger Syndrome.

作者信息

Grech Leanne, Mifsud Adrian, Caruana Maryanne, Carbonaro Francis

机构信息

Mater Dei Hospital, Msida, Malta.

出版信息

Case Rep Ophthalmol Med. 2017;2017:5808047. doi: 10.1155/2017/5808047. Epub 2017 Oct 23.

DOI:10.1155/2017/5808047
PMID:29201477
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5672606/
Abstract

Eisenmenger syndrome refers to reversal of shunt and central cyanosis due to pulmonary hypertension induced by congenital heart disease with a large systemic-to-pulmonary shunt. We report a case of a 17-year-old man with Eisenmenger syndrome who presented with gradual deterioration in visual acuity and was diagnosed with advanced secondary open angle glaucoma. There have been reports of patients suffering from thrombosis due to hyperviscosity associated with this syndrome; however, to our knowledge, the association of secondary open angle glaucoma with Eisenmenger syndrome has not yet been documented.

摘要

艾森曼格综合征是指由于先天性心脏病导致体循环至肺循环大量分流,进而引起肺动脉高压,导致分流逆转和中心性发绀。我们报告一例17岁艾森曼格综合征男性患者,该患者视力逐渐下降,被诊断为晚期继发性开角型青光眼。有报道称该综合征患者因血液高黏滞性而发生血栓形成;然而,据我们所知,继发性开角型青光眼与艾森曼格综合征之间的关联尚未见文献记载。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f788/5672606/4d848df90ea3/CRIOPM2017-5808047.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f788/5672606/6f20a38ded0d/CRIOPM2017-5808047.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f788/5672606/91231eb7b7a6/CRIOPM2017-5808047.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f788/5672606/4d848df90ea3/CRIOPM2017-5808047.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f788/5672606/6f20a38ded0d/CRIOPM2017-5808047.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f788/5672606/91231eb7b7a6/CRIOPM2017-5808047.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f788/5672606/4d848df90ea3/CRIOPM2017-5808047.003.jpg

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Dilated episcleral veins with secondary open angle glaucoma.巩膜扩张静脉伴继发性开角型青光眼。
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