Schaffert D A, Johnsen S D, Johnson P C, Drayer B P
Department of Neuropathology, St. Joseph's Hospital and Medical Center, Barrow Neurological Institute, Phoenix, AZ 85013.
Neurology. 1989 Mar;39(3):440-2. doi: 10.1212/wnl.39.3.440.
We present an 11-year-old girl in whom high field strength MRI performed 2 1/2 years and 6 months before her death showed prominent hypointensity in the globus pallidus and substantia nigra consistent with iron deposition. This finding suggested Hallervorden-Spatz disease, which was confirmed at autopsy.