Sethi K D, Adams R J, Loring D W, el Gammal T
Department of Neurology, Medical College of Georgia, Augusta 30912.
Ann Neurol. 1988 Nov;24(5):692-4. doi: 10.1002/ana.410240519.
Two women with a presumptive diagnosis of Hallervorden-Spatz syndrome had a combination of dystonia and parkinsonism. One had retinitis pigmentosa. Neuropsychological testing revealed decreased verbal fluency and visuoconstructional and motor deficits. Magnetic resonance imaging performed with a high-field-strength unit (1.5 Tesla) showed striking abnormalities in the globus pallidus bilaterally ("eye-of-the-tiger" sign). Magnetic resonance imaging may prove useful in the diagnosis of Hallervorden-Spatz syndrome.
两名初步诊断为哈勒沃登-施帕茨综合征的女性出现了肌张力障碍和帕金森综合征的症状。其中一名患有色素性视网膜炎。神经心理学测试显示语言流畅性下降以及视觉构建和运动功能缺陷。使用高场强设备（1.5特斯拉）进行的磁共振成像显示双侧苍白球有明显异常（“虎眼征”）。磁共振成像可能对哈勒沃登-施帕茨综合征的诊断有用。
