Ambrus Nóra, Havasi Kálmán, Kalapos Anita, Sághy László, Makai Attila, Bogáts Gábor, Hegedűs Zoltán, Iványi Béla, Besenyi Zsuzsanna, Pápai Zsuzsanna, Nagy László, Forster Tamás, Nemes Attila
Faculty of Medicine, Second Department of Medicine and Cardiology Center, Albert Szent-Györgyi Clinical Centre, University of Szeged, Szeged, Hungary.
Faculty of Medicine, Second Department of Medicine and Cardiology Center, Division of Cardiac Surgery, Albert Szent-Györgyi Clinical Centre, University of Szeged, Szeged, Hungary.
Echocardiography. 2018 Feb;35(2):267-271. doi: 10.1111/echo.13808. Epub 2018 Jan 19.
Cardiac angiosarcomas are the most common primary malignant cardiac tumors in adults. The diagnosis is often delayed due to nonspecific clinical symptoms at presentation. The cornerstones of diagnosis are echocardiography and the histological evaluation of the cardiac biopsy. The knowledge on the treatment is limited; the outcomes of chemotherapy, radiotherapy, complete surgical removal, and heart transplantation are controversial. We report a 38-year-old woman with a primary heart tumor which infiltrated the right atrial wall and the pericardium and caused pericardial effusion. Angiosarcoma was verified histologically. The surgical excision could not be radical, and the patient died 3 months from diagnosis.
心脏血管肉瘤是成人中最常见的原发性恶性心脏肿瘤。由于发病时临床症状不具特异性,诊断往往会延迟。诊断的基石是超声心动图和心脏活检的组织学评估。关于治疗的知识有限;化疗、放疗、完整手术切除和心脏移植的结果存在争议。我们报告一名38岁女性,患有原发性心脏肿瘤,该肿瘤浸润右心房壁和心包并导致心包积液。组织学证实为血管肉瘤。手术切除无法根治,患者在确诊后3个月死亡。