Wessell Aaron, Hersh David S, Ho Cheng-Ying, Lumpkins Kimberly M, Groves Mari L A
Department of Neurosurgery, University of Maryland School of Medicine, Baltimore, MD, USA.
Department of Pathology, University of Maryland School of Medicine, Baltimore, MD, USA.
Childs Nerv Syst. 2018 May;34(5):977-982. doi: 10.1007/s00381-018-3718-9. Epub 2018 Jan 24.
Type IV sacrococcygeal teratoma with intraspinal involvement is rare and to our knowledge has not been reported previously in the literature. The authors present the case of a 2-month-old infant with a type IV sacrococcygeal teratoma diagnosed on prenatal ultrasound. Postnatal MRI revealed intraspinal extension through an enlarged sacral neuroforamina on the right side. On surgical exploration, the authors discovered a dorsal cystic tumor involving the sacral spine that extended through an enlarged S4 foramen to a large presacral component. The tumor was successfully removed to achieve a complete en bloc surgical resection. The authors review the epidemiology, pathophysiology, and treatment of sacrococcygeal teratomas with intraspinal extension.
伴有脊髓受累的IV型骶尾部畸胎瘤很罕见，据我们所知，此前文献中尚未有过报道。作者报告了一例产前超声诊断为IV型骶尾部畸胎瘤的2个月大婴儿病例。产后MRI显示肿瘤通过右侧扩大的骶神经孔向脊髓内延伸。手术探查时，作者发现一个累及骶骨的背侧囊性肿瘤，该肿瘤通过扩大的S4孔延伸至一个巨大的骶前部分。肿瘤被成功切除，实现了完整的整块手术切除。作者回顾了伴有脊髓内延伸的骶尾部畸胎瘤的流行病学、病理生理学和治疗方法。
