Munjal Satyashiva, Srivastava Amit, Tucker Shivya, Bakshi Neha, Bhalla Sunita, Mehta V S
Department of Neurosurgery, Paras Hospital, Gurgaon, Haryana, India.
Department of Radiology, Moolchand Medcity, New Delhi, India.
J Craniovertebr Junction Spine. 2017 Oct-Dec;8(4):378-381. doi: 10.4103/jcvjs.JCVJS_70_17.
Primary spinal primitive neuroectodermal tumor (psPNET) is a rare entity with few cases reported in literature. We report a case of a 50-year-old female who presented to us with paraplegia and was diagnosed with extradural dorsal spine psPNET. The diagnosis was not suspected at presentation or on radiology but was established on histopathological examination. It is important to distinguish it from central nervous system primitive neuroectodermal tumors and from other spinal tumors since it follows a different clinical course and therapeutic outcome.
原发性脊髓原始神经外胚层肿瘤(psPNET)是一种罕见的疾病,文献报道的病例很少。我们报告一例50岁女性,因截瘫前来就诊,被诊断为硬脊膜外背侧脊柱psPNET。就诊时或影像学检查时均未怀疑该诊断,而是通过组织病理学检查确诊。将其与中枢神经系统原始神经外胚层肿瘤及其他脊柱肿瘤区分开来很重要,因为它们的临床病程和治疗结果不同。