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2型H型或小胆管重复胆囊的产前及准确围产期诊断。

Prenatal and accurate perinatal diagnosis of type 2 H or ductular duplicate gallbladder.

作者信息

Maggi Umberto, Farris Giorgio, Carnevali Alessandra, Borzani Irene, Clerici Paola, Agosti Massimo, Rossi Giorgio, Leva Ernesto

机构信息

UOC Chirurgia Pediatrica, Centro Trapianti Fegato - Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico di Milano, V Francesco Sforza 35, 20121, Milan, Italy.

UO Chirurgia Epatobiliopancreatica e trapianti di fegato, Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico di Milano, Milan, Italy.

出版信息

BMC Pediatr. 2018 Feb 7;18(1):38. doi: 10.1186/s12887-018-1043-9.

Abstract

BACKGROUND

Double gallbladder is a rare biliary anomaly. Perinatal diagnosis of the disorder has been reported in only 6 cases, and in 5 of them the diagnosis was based on ultrasound imaging only. However, the ultrasound technique alone does not provide a sufficiently precise description of cystic ducts and biliary anatomy, an information that is crucial for a correct classification and for a possible future surgery.

CASE PRESENTATION

At 21 weeks of gestational age of an uneventful pregnancy in a 38 year old primipara mother, a routine ultrasound screening detected a biliary anomaly in the fetus suggestive of a double gallbladder. A neonatal abdominal ultrasonography performed on postnatal day 2 confirmed the diagnosis. On day 12 the newborn underwent a Magnetic Resonance Cholangiopancreatography (MRCP) that clearly characterized the anatomy of the anomaly: both gallbladders had their own cystic duct and both had a separate insertion in the main biliary duct.

CONCLUSIONS

We report a case of early prenatal suspected duplicate gallbladder that was confirmed by a neonatal precise diagnosis of a Type 2, H or ductular duplicate gallbladder, using for the first time 3D images of Magnetic resonance cholangiopancreatography in a newborn. An accurate anatomical diagnosis is mandatory in patients undergoing a possible future cholecystectomy, to avoid surgical complications or reoperations. Therefore, in case of a perinatal suspicion of a double gallbladder, neonates should undergo a Magnetic resonance cholangiopancreatography. A review of the Literature about this variant is included.

摘要

背景

双胆囊是一种罕见的胆道畸形。围产期诊断出该疾病的报道仅有6例,其中5例的诊断仅基于超声成像。然而,仅靠超声技术无法充分精确地描述胆囊管和胆道解剖结构,而这些信息对于正确分类以及未来可能进行的手术至关重要。

病例报告

一名38岁初产妇妊娠过程顺利,在孕21周时,常规超声筛查发现胎儿存在提示双胆囊的胆道畸形。出生后第2天进行的新生儿腹部超声检查确诊了该诊断。在第12天,新生儿接受了磁共振胰胆管造影(MRCP),该检查清晰地显示了畸形的解剖结构:两个胆囊都有各自的胆囊管,且都分别汇入主胆管。

结论

我们报告了一例产前早期疑似重复胆囊的病例,该病例通过新生儿对2型、H型或导管型重复胆囊的精确诊断得以确诊,首次在新生儿中使用了磁共振胰胆管造影的三维图像。对于可能未来要进行胆囊切除术的患者,准确的解剖诊断是必不可少的,以避免手术并发症或再次手术。因此,在围产期怀疑双胆囊的情况下,新生儿应接受磁共振胰胆管造影检查。本文还包括了关于该变异的文献综述。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bd32/5803916/3525394d3f68/12887_2018_1043_Fig1_HTML.jpg

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