家族性掌跖角化症中的心脏异常
Cardiac abnormalities in familial palmoplantar keratosis.
作者信息
Protonotarios N, Tsatsopoulou A, Patsourakos P, Alexopoulos D, Gezerlis P, Simitsis S, Scampardonis G
出版信息
Br Heart J. 1986 Oct;56(4):321-6. doi: 10.1136/hrt.56.4.321.
Abstract
Cardiac abnormalities were identified in patients with familial palmoplantar keratosis. All of them were descended from families on the Greek island of Naxos. Four families were studied and nine cases of palmoplantar keratosis were identified; seven of them showed symptoms and signs of heart disease. Cardiomegaly on chest x ray and electrocardiographic abnormalities were common findings. Three cases had episodes of ventricular tachycardia and a fourth patient died suddenly. All patients with cardiac signs and symptoms showed echocardiographic enlargement of the right ventricle and a right ventricular band; in three the left ventricle was also affected.
摘要
在家族性掌跖角化病患者中发现了心脏异常。他们均来自希腊纳克索斯岛的家族。研究了四个家族，共识别出9例掌跖角化病；其中7例有心脏病的症状和体征。胸部X光显示心脏扩大和心电图异常是常见表现。3例出现室性心动过速发作，第四例患者突然死亡。所有有心脏体征和症状的患者超声心动图均显示右心室扩大和右心室束带；3例左心室也受到影响。
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