Song Yu-Xin, Wang Zeng-Ping, Liu Lin, Xue Wen, Hao Zhong-Yu, Zhang Qun-Li, She Wei, Cai Li-Yang, Gou Hai-Tao, Qian Yao-Wen
The 2nd Department of Orthopaedics, Gansu Provincial Hospital, Lanzhou 730000, Gansu, China.
The 2nd Department of Orthopaedics, Gansu Provincial Hospital, Lanzhou 730000, Gansu, China;
Zhongguo Gu Shang. 2017 Oct 25;30(10):976-978. doi: 10.3969/j.issn.1003-0034.2017.10.020.
Madelung deformity is a rare deformity of forearm and wrist caused by growth disorders of distal radius ulnar and palmar epiphyseal. Current studies showed that its incidence mainly associated with trauma, epiphyseal developmental abnormalities, nutritional disorders and genetic deletion or mutation. The early clinical presentation is not typical, in middle and late time, wrist deformity and weak can appear. Plain film considered as the main means of diagnosis is often lack of early diagnosis significance. Although wrist joint magnetic resonance imaging showing early soft tissue and skeletal abnormalities were used for the early diagnosis of the disease, current domestic study in magnetic resonance imaging of this deformity is less. According to the size of the distal ulnar inclination angle and palm angle, this deformity can be divided into different types. The patients with severe deformity and symptoms usually need surgical intervention including ulna revision and osteotomy of the distal radius at present. Although the two operation can achieve good clinical results, the surgical trauma, infection and postoperative risk of joint activities are more.
马德隆畸形是一种由桡尺远侧和掌侧骨骺生长紊乱引起的罕见的前臂和腕部畸形。目前的研究表明，其发病率主要与创伤、骨骺发育异常、营养障碍以及基因缺失或突变有关。早期临床表现不典型，中晚期可出现腕部畸形和无力。X线平片虽被视为主要诊断手段，但往往缺乏早期诊断意义。尽管腕关节磁共振成像显示早期软组织和骨骼异常可用于该病的早期诊断，但目前国内关于这种畸形的磁共振成像研究较少。根据尺骨远端倾斜角和掌角的大小，这种畸形可分为不同类型。目前，畸形严重且有症状的患者通常需要手术干预，包括尺骨矫正和桡骨远端截骨术。尽管这两种手术能取得良好的临床效果，但手术创伤、感染以及术后关节活动风险较大。
