Bhattar Rohit, Tomar Vinay, Dhakad Devendra Singh, Agarwal Neeraj
Department of Urology, Sawai Man Singh Medical College, Jaipur, Rajasthan.
Turk J Urol. 2018 Jan;44(1):87-90. doi: 10.5152/tud.2017.26780. Epub 2017 Dec 19.
Neurilemmomas are benign, slow growing, encapsulated nerve sheath tumor. These tumors arise from the schwann cells of neural crest. Neurilemmomas can manifest in various form according to site, extent and severity of involvement of organ. Diaphragmatic neurilemmomas are very unusual and even difficult to diagnose on preoperative imaging. We will report a case of 39 year old male, who presented with complaints of occasional left flank pain for one year and subsequently investigated, which showed left adrenal cyst with haemorrhagic fluid content. On the contrary, when surgical exploration of the lesion was done, it showed a cyst within the diaphragm, completely separated from left kidney and left adrenal with haemorrhagic content in situ. Histopathological examination of the lesion showed it to be a benign neurilemmoma with cystic degeneration. Post opearatively patient did well. We believe that this is the first case report, which is addressing such kind of initial manifestation of diaphragmatic neurilemmomas.
神经鞘瘤是一种良性、生长缓慢、有包膜的神经鞘肿瘤。这些肿瘤起源于神经嵴的施万细胞。神经鞘瘤可根据受累器官的部位、范围和严重程度以各种形式表现出来。膈神经鞘瘤非常罕见,术前影像学检查甚至难以诊断。我们将报告一例39岁男性患者,该患者主诉偶尔左侧胁腹疼痛一年,随后进行检查,结果显示左肾上腺囊肿,囊内为血性液体。相反,当对病变进行手术探查时,发现膈肌内有一个囊肿,与左肾和左肾上腺完全分离,囊内为原位血性内容物。病变的组织病理学检查显示为伴有囊性变的良性神经鞘瘤。术后患者恢复良好。我们认为这是第一例报道膈神经鞘瘤这种初始表现的病例报告。