Chen Chao-Bo, Hu Wei-Dong, Zhao Wan-Wen, Gu Yan-Yan, Hou Hong-Wei, Pan Zheng
Department of General Surgery, Wuxi Xishan People's Hospital, Wuxi, China.
Department of General Surgery, Zhongda Hospital, Southeast University, Nanjing, China.
Ann Surg Treat Res. 2018 Mar;94(3):162-165. doi: 10.4174/astr.2018.94.3.162. Epub 2018 Feb 28.
Caroli disease is a rare congenital disorder characterized by nonobstructive dilatation of intrahepatic ducts. In cases with symptomatic intrahepatic manifestations, treatment should correspond to the type with hepatic resection for localized disease and transplantation for diffuse forms. If possible, complete resection of the cysts can cure the symptoms and avoid the risk of malignancy. A 66-year-old woman presented to Wuxi Xishan People's Hospital with recurrent intermittent upper quadrant abdominal pain. Further examinations suggested the diagnosis of Caroli disease limited to the left hepatic lobe. She underwent laparoscopic hepatectomy. Pathological examination confirmed the diagnosis of Caroli disease, and no malignancy was found. There were no immediate complications and no long-term complications after one and one-half years of follow-up. Laparoscopic hepatectomy could be a feasible, safe treatment option for localized Caroli disease.
卡罗里病是一种罕见的先天性疾病,其特征为肝内胆管非梗阻性扩张。对于有症状的肝内表现的病例,治疗应根据类型进行,局限性疾病采用肝切除术,弥漫性形式采用移植术。如果可能,完整切除囊肿可治愈症状并避免恶性肿瘤风险。一名66岁女性因反复间歇性上腹部疼痛就诊于无锡市锡山人民医院。进一步检查提示诊断为局限于左肝叶的卡罗里病。她接受了腹腔镜肝切除术。病理检查确诊为卡罗里病,未发现恶性肿瘤。术后无即刻并发症,随访一年半后也无长期并发症。腹腔镜肝切除术对于局限性卡罗里病可能是一种可行、安全的治疗选择。