Karray O, Boulma R, Abdi A, Ben Miled A, Dhaoui A, Menif N, Bellil K, Khouni H, Chouchen A
Urology Unit, Interior Security Forces Hospital, La Marsa, Tunisia.
General Surgery Department, Interior Security Forces Hospital, La Marsa, Tunisia.
J Med Case Rep. 2018 Mar 26;12(1):81. doi: 10.1186/s13256-018-1617-z.
Leiomyomas are benign tumors observed mainly in adult women. The retroperitoneum is a rare location for leiomyomas; almost 100 cases have been reported. Because retroperitoneal leiomyomas are paucisymptomatic and the tumor size at diagnosis is relatively large, surgical management is challenging. Regular follow-up is required because recurrence and malignant sarcomatous transformation have been described in a few cases.
We report a case of a 52-year-old North African woman with a 22-cm retroperitoneal leiomyoma. A preoperative embolization was performed 2 days before surgery. The clinical, therapeutic, and evolutive aspects of this rare entity are discussed.
Despite its benignity, retroperitoneal leiomyoma is a challenging diagnostic, therapeutic, and evolutive condition. Surgeons must consider mainly the tumor's vascularization. Regular follow-up is mandatory because malignant transformation cannot be excluded.
平滑肌瘤是主要见于成年女性的良性肿瘤。腹膜后是平滑肌瘤的罕见部位；已报道了近100例。由于腹膜后平滑肌瘤症状较少，且诊断时肿瘤体积相对较大，手术治疗具有挑战性。少数病例中已描述有复发和恶性肉瘤样变，因此需要定期随访。
我们报告一例52岁的北非女性，患有一个22厘米的腹膜后平滑肌瘤。术前2天进行了栓塞。讨论了这种罕见疾病的临床、治疗及演变情况。
尽管腹膜后平滑肌瘤为良性，但在诊断、治疗及病情演变方面均具有挑战性。外科医生必须主要考虑肿瘤的血管形成情况。由于不能排除恶性转化，定期随访是必需的。
