Kumar Rajnish, Kumari Bibha
Department of Anaesthesiology, IGIMS, Patna, Bihar, India.
Anesth Essays Res. 2018 Jan-Mar;12(1):271-272. doi: 10.4103/aer.AER_208_17.
Hypertrophic cardiomyopathy (HCM) is a genetic myocardial disease usually characterized by asymmetric ventricular septal hypertrophy. HCM is an important cause of sudden cardiac death in adolescents and young adults. We are presenting a case report, ten years boy came in emergency with sudden loss of consciousness (witness cardiac arrest). Child was revived after cardiopulmonary resuscitation and send to coronary care unit. Echocardiography findings were suggestive of HCM. There was history of sudden death of her mother and maternal uncle. After stabilization ICD was implanted under total intravenous anesthesia. Post procedure his hospital stay was uneventful.
肥厚型心肌病(HCM)是一种遗传性心肌疾病,通常以不对称性室间隔肥厚为特征。HCM是青少年和青年人心源性猝死的重要原因。我们现报告一例,一名10岁男孩因突发意识丧失(目击者称心脏骤停)前来急诊。经心肺复苏后患儿恢复自主循环,并被送往冠心病监护病房。超声心动图检查结果提示为HCM。其母亲和舅舅有猝死病史。病情稳定后,在全静脉麻醉下植入了植入式心律转复除颤器(ICD)。术后他在医院的恢复过程顺利。