Chaudhary Meenu, Shah D N, Chaudhary R P
Nepal J Ophthalmol. 2017 Jul;9(18):170-174. doi: 10.3126/nepjoph.v9i2.19261.
Takayasu's disease (TD) (pulseless disease, aortic arch syndrome) is a rare but potentially life-threatening chronic giant cell vasculitis. The major complications attributed to the disease include Takayasu's retinopathy, secondary hypertension, aortic regurgitation, and arterial aneurysm. The aim of this study is to describe a patient with Takayasu's disease and scleritis and to show its association.
We describe a 44-year-old female patient with Takayasu's disease who presented with bilateral anterior scleritis in the form of painful red eye. Patient did not have any associated autoimmune diseases. Patient was diagnosed to have TD and was treated with immunosuppressant.
Scleritis though rare can be a vasculitic feature of TD. This is a first report of Takayasu's disease with scleritis, which has been documented in Nepal.
高安氏病（TD）（无脉症、主动脉弓综合征）是一种罕见但可能危及生命的慢性巨细胞血管炎。该疾病的主要并发症包括高安氏视网膜病变、继发性高血压、主动脉反流和动脉动脉瘤。本研究的目的是描述一名患有高安氏病和巩膜炎的患者，并展示两者之间的关联。
我们描述了一名44岁患有高安氏病的女性患者，她表现为双眼前部巩膜炎，症状为眼睛疼痛发红。患者没有任何相关的自身免疫性疾病。患者被诊断为高安氏病，并接受了免疫抑制剂治疗。
巩膜炎虽然罕见，但可能是高安氏病的血管炎特征。这是尼泊尔首次报道的高安氏病合并巩膜炎的病例。
