Lewis V D, Meranze S G, McLean G K, O'Neill J A, Berkowitz H D, Burke D R
Department of Radiology, Hospital of the University of Pennsylvania, Philadelphia 19104.
Radiology. 1988 Apr;167(1):111-3. doi: 10.1148/radiology.167.1.2964673.
The midaortic syndrome is an unusual entity seen in children and adolescents. It is characterized by severe narrowing of the abdominal aorta with progressive involvement of the renal and visceral branches. Eleven patients (aged 5 months to 15 years) suspected of having midaortic syndrome were examined preoperatively and postoperatively. All patients had hypertension and were examined with midstream aortography. All aortograms showed a smooth, segmental stenosis of the abdominal aorta and severe bilateral proximal renal artery stenosis. In three patients, percutaneous transluminal angioplasty of the renal artery was attempted, two preoperatively and one for a postoperative stricture. None showed long-term success, presumably due to the progressive nature of the disease. Grafts were surgically placed in ten patients and produced successful results in nine.
中段主动脉综合征是一种在儿童和青少年中出现的罕见病症。其特征为腹主动脉严重狭窄，并逐渐累及肾动脉和内脏分支。对11例疑似患有中段主动脉综合征的患者（年龄5个月至15岁）进行了术前和术后检查。所有患者均患有高血压，并接受了腹主动脉造影检查。所有主动脉造影均显示腹主动脉呈光滑的节段性狭窄以及双侧肾动脉近端严重狭窄。对3例患者尝试进行了经皮腔内肾动脉血管成形术，其中2例在术前进行，1例针对术后狭窄。无一例取得长期成功，推测是由于该疾病的进展性。10例患者接受了手术植入移植物，9例取得了成功结果。
