Goyal Pradeep, Motiwala Henal, Gupta Nishant, Gupta Sonali, Bansal Itisha, Hooda Kusum, Kumar Yogesh, Olsavsky Thomas D
Department of Radiology, Saint Vincent's Medical Center, Bridgeport, CT, U.S.A.
Frank H. Netter M.D. School of Medicine at Quinnipiac University, North Haven, CT, U.S.A.
Pol J Radiol. 2017 Oct 20;82:616-620. doi: 10.12659/PJR.902677. eCollection 2017.
Poland syndrome (PS) is a rare congenital anomaly associated with absent or hypoplastic pectoralis major muscle and a wide spectrum of ipsilateral thoracic and upper extremity deformities. Hidradenitis suppurativa (HS) is a recurrent inflammatory follicular disease that commonly affects the apocrine-bearing skin and involves follicular occlusion and hyperkeratosis.
We report a case of a 46-year-old male with a history of chronic recurrent hidradenitis suppurativa who was incidentally found to have a simple type of Poland syndrome with incidental hypoplasia of ipsilateral gluteal muscles.
Not only can PS present with HS, which we describe for the first time, but it is also associated with a wide variability of symptoms such as previously unknown co-existence of gluteal muscles hypoplasia.
波兰综合征(PS)是一种罕见的先天性异常,与胸大肌缺如或发育不全以及同侧胸部和上肢的广泛畸形有关。化脓性汗腺炎(HS)是一种复发性炎症性毛囊疾病,通常影响含顶泌汗腺的皮肤,涉及毛囊阻塞和角化过度。
我们报告一例46岁男性,有慢性复发性化脓性汗腺炎病史,偶然发现患有单纯型波兰综合征,同侧臀肌偶然发育不全。
PS不仅可伴有HS(我们首次描述),还与多种症状有关,如先前未知的臀肌发育不全并存。