Doan Ninh Ba, Patel Mohit, Nguyen Ha Son, Janich Karl, Montoure Andrew, Shabani Saman, Gelsomino Michael
Department of Neurosurgery, Medical College of Wisconsin, Milwaukee, Wisconsin, 53226, USA.
Asian J Neurosurg. 2018 Apr-Jun;13(2):475-477. doi: 10.4103/1793-5482.228563.
Medulloblastomas are categorized as the World Health Organization Grade IV neoplasms. Only 33 cases have been reported of extra-axial, mostly in the cerebellar pontine angle and lateral cerebellar hemisphere, medulloblastomas in the current literature. Our study showcases the first case of an extremely rare presentation of an extra-axial midline tentorial adult medulloblastoma with the dural-tail sign mimicking a meningioma. To achieve the best possible outcome, a high index of suspicion for medulloblastoma is critical especially in young patient with an atypical posterior fossa mass as treatment regimens drastically different between a medulloblastoma and a meningioma.
髓母细胞瘤被归类为世界卫生组织IV级肿瘤。在当前文献中,仅报道了33例轴外髓母细胞瘤,大多位于小脑脑桥角和小脑半球外侧。我们的研究展示了首例极其罕见的轴外中线小脑幕成人髓母细胞瘤,其硬脑膜尾征酷似脑膜瘤。为了获得最佳治疗效果,对髓母细胞瘤保持高度怀疑指数至关重要,尤其是对于患有非典型后颅窝肿块的年轻患者,因为髓母细胞瘤和脑膜瘤的治疗方案截然不同。