Lábadi Beatrix, Beke Anna Maria
Pécsi Tudományegyetem, Bölcsészettudományi Kar, Pszichológia Intézet, Péc.
Semmelweis Egyetem, I. Sz. Szülészeti és Nôgyógyászati Klinika, Budapest.
Ideggyogy Sz. 2016 Nov 30;69(11-12):373-379. doi: 10.18071/isz.69.0373.
Agenesis of corpus callosum is a relatively frequent congenital cerebral malformation including dysplasia, total or partial absence of corpus callosum. The agenesis of corpus callosum can be occured in isolated form without accompanying somatic or central nervous system abnormalities and it can be associated with other central nervus system malformations. The behavioral and cognitive outcome is more favorable for patients with isolated agenesis of corpus callous than syndromic form of corpus callosum. The aim of this study is to review recent research on behavioral and social-cognitive functions in individuals with agenesis of corpus callosum. Developmental delay is common especially in higher-order cognitive and social functions.
An internet database search was performed to identify publications on the subject.
Fifty-five publications in English corresponded to the criteria. These studies reported deficits in language, social cognition and emotions in individuals with agenesis of corpus callosum which is known as primary corpus callous syndrome.
The results indicate that individuals with agenesis of corpus callosum have deficiency in social-cognitive domain (recognition of emotions, weakness in paralinguistic aspects of language and mentalizing abilities). The impaired social cognition can be manifested in behavioral problems like autism and attention deficit hyperactivity disorder.
胼胝体发育不全是一种相对常见的先天性脑畸形，包括发育异常、胼胝体完全或部分缺失。胼胝体发育不全可单独出现，不伴有躯体或中枢神经系统异常，也可与其他中枢神经系统畸形相关。与综合征型胼胝体发育不全患者相比，孤立性胼胝体发育不全患者的行为和认知结局更为良好。本研究的目的是综述近期关于胼胝体发育不全个体行为和社会认知功能的研究。发育迟缓很常见，尤其是在高阶认知和社会功能方面。
通过互联网数据库搜索来识别关于该主题的出版物。
55篇英文出版物符合标准。这些研究报告了胼胝体发育不全个体在语言、社会认知和情感方面存在缺陷，这被称为原发性胼胝体综合征。
结果表明，胼胝体发育不全个体在社会认知领域存在缺陷（情绪识别、语言副语言方面的弱点和心理理论能力）。社会认知受损可表现为自闭症和注意力缺陷多动障碍等行为问题。
