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J Assist Reprod Genet. 2018 Jun;35(6):953-964. doi: 10.1007/s10815-018-1197-2. Epub 2018 May 9.
VACTERL, the prototype for associated congenital anomalies, also has connections with functional issues such as pregnancy losses, prematurity, growth delays, perinatal difficulties, and parental subfertility. This segues into a broader association with similar connections even in the absence of malformations. DNA methylation disturbances in the ovum are a likely cause, with epigenetic links to individual components and to folate effects before conception, explaining diverse fetal and placental findings and providing a link to fetal origin hypothesis-related effects. The association encompasses the following: (1) Pre- and periconceptual effects, with frequent fertility issues and occasional imprinting disorders. (2) Early malformations. (3) Adverse pregnancy outcomes (APOs), as above. (4) Developmental destabilization that resolves soon after birth. This potentiates other causes of association findings, introducing multiple confounders. (5) Long-term fetal origins hypothesis-related risks. The other findings are exceptional when the same malformations have Mendelian origins, supporting a distinct pathogenesis. Expressions are facilitated by one-carbon metabolic issues, maternal and fetal stress, and decreased embryo size. This may be one of the commonest causes of adverse reproductive outcomes, but multifactorial findings, variable onsets and phenotypes, and interactions with multiple confounders make recognition difficult. This association supports VACTERL as a continuum that includes isolated malformations, extends the fetal origins hypothesis, explains adverse effects linked to maternal obesity, and suggests possible interventions.
VACTERL 是先天性畸形相关的原型,也与妊娠丢失、早产、生长迟缓、围产期困难和父母生殖力低下等功能问题有关。这就引出了一个更广泛的关联,即使没有畸形也存在类似的关联。卵子中的 DNA 甲基化紊乱是一个可能的原因,与个体成分和受孕前叶酸的影响有表观遗传联系,解释了不同的胎儿和胎盘发现,并为与胎儿起源假说相关的影响提供了联系。这种关联包括以下几个方面:(1) 前和围孕期的影响,常伴有生育问题和偶尔的印迹障碍。(2) 早期畸形。(3) 上述不良妊娠结局 (APO)。(4) 出生后不久即解决的发育不稳定。这会增强关联发现的其他原因,引入多种混杂因素。(5) 长期与胎儿起源假说相关的风险。当相同的畸形具有孟德尔起源时,其他发现是异常的,支持一种独特的发病机制。这些发现是由一碳代谢问题、母婴压力和胚胎大小减小促进的。这可能是不良生殖结果最常见的原因之一,但多因素发现、可变的发病和表型以及与多种混杂因素的相互作用使识别变得困难。这种关联支持 VACTERL 是一个连续体,包括孤立的畸形,扩展了胎儿起源假说,解释了与母亲肥胖相关的不良影响,并提出了可能的干预措施。