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表现为神经根病的小儿骶骨髓样肉瘤:一种罕见的髓系白血病复发形式

Sacral Myeloid Sarcoma Manifesting as Radiculopathy in a Pediatric Patient: An Unusual Form of Myeloid Leukemia Relapse.

作者信息

Rodrigues Joana Ruivo, Brito Manuel João, Pais Rui Pedro Faria, Carvalho Sílvia

机构信息

Radiology Unit, Medical Imaging Department, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.

Pediatric Oncology Department, Hospital Pediátrico, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal.

出版信息

Case Rep Radiol. 2018 May 15;2018:4257012. doi: 10.1155/2018/4257012. eCollection 2018.

Abstract

Myeloid sarcoma (MS), granulocytic sarcoma or chloroma, is defined as a localized extramedullary mass of blasts of granulocytic lineage with or without maturation, occurring outside the bone marrow. MS can be diagnosed concurrently with acute myeloid leukemia (AML) or myelodysplastic syndrome (MDS). The authors report a case of sacral MS occurring as a relapse of myeloid leukemia in a 5-year-old girl who was taken to the emergency department with radiculopathy symptoms.

摘要

髓系肉瘤(MS),又称粒细胞肉瘤或绿色瘤,定义为粒细胞系原始细胞的局限性髓外肿块,可伴有或不伴有成熟,发生于骨髓外。MS可与急性髓系白血病(AML)或骨髓增生异常综合征(MDS)同时诊断。作者报告了一例5岁女孩骶骨MS病例,该病例为髓系白血病复发,因神经根病症状被送往急诊科。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4f1e/5977050/e395bd5fe9f3/CRIRA2018-4257012.001.jpg

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