Department of Ophthalmology, Hospital Civil Fray Antonio Alcalde, Guadalajara, México ; and.
Clínica oftalmológica Santa Lucía, Guadalajara, México .
Retin Cases Brief Rep. 2021 Mar 1;15(2):135-138. doi: 10.1097/ICB.0000000000000753.
To report a case of central retinal artery occlusion in a patient with macular telangiectasia Type 2 using multimodal imaging.
Observational case report.
A 58-year-old woman who presented with acute painless unilateral vision loss was diagnosed with central retinal artery occlusion in her right eye with macular telangiectasia Type 2 findings in both eyes. Fundus examination revealed retinal whitening with unusual cherry-red spot plus small crystalline deposits in the temporal macula. Surprisingly, spectral domain optical coherence tomography of the contralateral eye showed characteristically intraretinal hyporreflective spaces, whereas optical coherence tomography angiography exhibited microvascular abnormalities in the deep capillary plexus. At follow-up, a pseudolamellar macular hole was noticed in the affected eye with no recovery of best-corrected visual acuity.
This case describes an onset of central artery occlusion in a patient with underlying macular telangiectasia Type 2 and suggests that it had a possible role in the acceleration of its natural course. The utility of multimodal imaging lies on better accuracy in diagnosis as well as prognosis, management, and monitoring of the disease.
通过多模态成像报告一例 2 型黄斑毛细血管扩张症患者的视网膜中央动脉阻塞病例。
观察性病例报告。
一名 58 岁女性因急性无痛性单侧视力丧失就诊，右眼被诊断为视网膜中央动脉阻塞，双眼均有 2 型黄斑毛细血管扩张症表现。眼底检查显示视网膜苍白，伴有不寻常的樱桃红斑加上颞侧黄斑的小结晶状沉积物。令人惊讶的是，对侧眼的频域光相干断层扫描显示出特有的视网膜内低反射空间，而光相干断层血管造影显示深层毛细血管丛存在微血管异常。随访时，受累眼出现假性板层黄斑裂孔，最佳矫正视力无恢复。
本病例描述了一例潜在黄斑毛细血管扩张症 2 型患者的中央动脉阻塞发作，并提示其可能在加速其自然病程中起作用。多模态成像的应用在于提高诊断、预后、管理和监测疾病的准确性。
