Guedes Juliana Chaves Ruiz, Cunha Karen de Almeida Pinto Fernandes da, Machado Jorge Ricardo da Silva, Pinto Luciana Wernersbach
Service of Dermatology, Hospital Universitário Gaffrée e Guinle, Universidade Federal do Estado do Rio de Janeiro, Rio de Janeiro, RJ, Brazil.
Service of Dermatology, Instituto Nacional do Câncer, Rio de Janeiro, RJ, Brazil.
An Bras Dermatol. 2018 Jun;93(3):422-425. doi: 10.1590/abd1806-4841.20187097.
Extranodal NK/T-cell lymphoma nasal type is a rare disease that mainly affects the nasal cavity and paranasal sinuses of males in the fifth decade of life. It has aggressive and locally destructive behaviour, and can be complicated by the hemophagocytic syndrome, conferring high lethality to the disease. This article describes a case of NK/T-cell lymphoma nasal type in a previously healthy patient, exemplifying its rapid and fulminant course.
结外NK/T细胞淋巴瘤，鼻型是一种罕见疾病，主要影响50岁左右男性的鼻腔和鼻窦。它具有侵袭性和局部破坏性，可并发噬血细胞综合征，使该疾病具有高致死率。本文描述了一例既往健康患者发生的鼻型NK/T细胞淋巴瘤病例，例证了其快速且暴发性的病程。
