Imanishi Naoko, Takenaka Masaru, Nabe Yusuke, Nishimura Yosuke, Tanaka Fumihiro
Second Department of Surgery (Chest Surgery), University of Occupational and Environmental Health, Iseigaoka 1-1, Yahata-nishi-ku, Kitakyushu, 807-8555, Japan.
Department of Cardiovascular Surgery, University of Occupational and Environmental Health, Kitakyushu, Japan.
Gen Thorac Cardiovasc Surg. 2019 Mar;67(3):336-339. doi: 10.1007/s11748-018-0962-6. Epub 2018 Jun 22.
Vascular rings are congenital anomalies of the aortic arch, which may cause compression of the trachea and esophagus. Compression symptoms usually present in infants and children. Adult presentations are quite rare, and compression symptoms may not be relieved by surgical correction due to tracheal remodeling and malacia caused by a long-standing compression. Here, we present an adult case of symptomatic vascular ring formed by the right aortic arch and persistent left ligamentum arteriosus. Respiratory symptoms were predominantly due to severe tracheal stenosis caused by tracheal wall thickening through remodeling during long-standing compression, and were relieved by surgery with transection of the persistent followed by resection and reconstruction of the trachea.
血管环是主动脉弓的先天性异常,可导致气管和食管受压。压迫症状通常出现在婴幼儿和儿童中。成人病例相当罕见,由于长期压迫导致气管重塑和软化,手术矫正后压迫症状可能无法缓解。在此,我们报告一例由右位主动脉弓和永存左上腔静脉形成的有症状血管环的成人病例。呼吸症状主要是由于长期压迫导致气管壁通过重塑增厚而引起的严重气管狭窄,通过手术横断永存左上腔静脉,随后进行气管切除和重建得以缓解。