Lung Institute, University of Arizona, Banner University Medical Center, 755 E. McDowell Road, 3rd Floor, Phoenix, AZ 85006, USA.
Department of Respiratory Disease, Federico II University of Naples, Naples, Italy.
Heart Fail Clin. 2018 Jul;14(3):403-411. doi: 10.1016/j.hfc.2018.03.006.
Diffuse pulmonary lung disease and chronic obstructive pulmonary disease is a heterogeneous population that can manifest pulmonary hypertension. These subgroups are classified as primarily World Health Organization group 3. Available data suggest that the impact of pulmonary hypertension targeted therapy in diffuse pulmonary lung disease and chronic obstructive pulmonary disease is limited and survival is poor despite attempted treatment.
弥漫性肺疾病和慢性阻塞性肺疾病是一组异质性人群,可表现为肺动脉高压。这些亚组被归类为主要的世界卫生组织第 3 组。现有数据表明,尽管进行了治疗尝试,但靶向治疗弥漫性肺疾病和慢性阻塞性肺疾病相关肺动脉高压的效果有限,生存状况较差。