肾脏原发性低级别纤维黏液样肉瘤——一种极其罕见的疾病实体。
Primary Low-Grade Fibromyxoid Sarcoma of Kidney-an Extremely Rare Entity.
作者信息
Bhattar Rohit, Aggarwal S P, Yadav S S, Tomar V
机构信息
Department of Urology and Renal Transplantation, SMS Medical College, Jaipur, Rajasthan India.
出版信息
Indian J Surg. 2018 Jun;80(3):281-283. doi: 10.1007/s12262-017-1698-8. Epub 2017 Oct 29.
Renal LGFMS is an extremely rare tumor. So far, only four cases have been reported in literature. LGFMS are indolent tumor with distinctive histopathological features with potential for late recurrences and metastasis. The diagnosis is made on histopathological examination and supported by immunohistochemical analysis. A 35-year-old young male was presented with flank pain and lump and diagnosed as low-grade fibromyxoid sarcoma after surgery on immunohistochemical analysis. This is the fifth case of renal LGFMS and we presented the review of literature. Radical surgery remains the primary treatment modality. Long follow-up is mandatory.
肾脏低度恶性纤维黏液样肉瘤是一种极其罕见的肿瘤。迄今为止，文献中仅报道了4例。低度恶性纤维黏液样肉瘤是一种生长缓慢的肿瘤，具有独特的组织病理学特征，有晚期复发和转移的可能。诊断依靠组织病理学检查，并通过免疫组化分析予以支持。一名35岁的年轻男性因侧腹疼痛和肿块就诊，术后经免疫组化分析诊断为低度纤维黏液样肉瘤。这是第5例肾脏低度恶性纤维黏液样肉瘤，我们在此呈现文献综述。根治性手术仍然是主要的治疗方式。必须进行长期随访。
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